-
Uroporphyrinogens are
cyclic tetrapyrroles with four
propionic acid
groups ("P" groups) and four
acetic acid
groups ("A" groups).
There are four forms...
- not
cause severe illness. The
disorder results from a
deficiency of
uroporphyrinogen III decarboxylase, used in the
production of heme, a
vital component...
-
Uroporphyrinogen I is an
isomer of
uroporphyrinogen III, a
metabolic intermediate in the
biosynthesis of heme. A type of
porphyria is
caused by production...
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Uroporphyrinogen III
decarboxylase (
uroporphyrinogen decarboxylase, or UROD) is an
enzyme (EC 4.1.1.37) that in
humans is
encoded by the UROD gene. Uroporphyrinogen...
-
metabolic disorder affecting heme,
caused by
deficiency of the
enzyme uroporphyrinogen cosynthetase. It is
extremely rare, with a
prevalence estimated at...
-
Uroporphyrinogen III is a tetrapyrrole, the
first macrocyclic intermediate in the
biosynthesis of heme, chlorophyll,
vitamin B12, and siroheme. It is a...
-
Uroporphyrinogen III
synthase (EC 4.2.1.75) is an
enzyme involved in the
metabolism of the
cyclic tetrapyrrole compound porphyrin. It is
involved in the...
-
Uroporphyrinogen-III C-methyltransferase (EC 2.1.1.107),
uroporphyrinogen methyltransferase,
uroporphyrinogen-III methyltransferase, adenosylmethionine-uroporphyrinogen...
-
bilane (HMB),
which is
hydrolysed to form the
circular tetrapyrrole uroporphyrinogen III. This
molecule undergoes a
number of
further modifications. Intermediates...
- of
hepatic porphyria caused by a
disorder in both
genes which code
Uroporphyrinogen III
decarboxylase (UROD).: 525 It has a
similar presentation to porphyria...
