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Members of the
thiolase family can be
divided into two
broad categories:
degradative thiolases (EC 2.3.1.16) and
biosynthetic thiolases (EC 2.3.1.9). These...
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names 3-oxothiolase deficiency,
Mitochondrial acetoacetyl-coenzyme A
thiolase deficiency, Alpha-methyl-acetoacetyl-CoA
thiolase deficiency Isoleucine...
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enzyme subunit beta,
mitochondrial (TP-beta) also
known as 3-ketoacyl-CoA
thiolase, acetyl-CoA acyltransferase, or beta-ketothiolase is an
enzyme that in...
- Acetyl-CoA acetyltransferase, mitochondrial, also
known as acetoacetyl-CoA
thiolase, is an
enzyme that in
humans is
encoded by the ACAT1 (Acetyl-Coenzyme A...
- 2NADH + FADH2
Condensation of pair of
acetyl CoA
molecules as
catalyzed by
thiolase.: 393 2Ac−CoA → AcCH2C(O)−CoA + H−CoA In mammals,
acetoacetate produced...
- SCAD, MCAD, VLCAD, 3-hydroxyacyl-coenzyme A
dehydrogenase deficiency),
thiolase deficiency Mitochondrial myopathies:
deficiency of
succinate dehydrogenase...
-
mitochondrial also
known as hydroxyacyl-CoA dehydrogenase/3-ketoacyl-CoA
thiolase/enoyl-CoA
hydratase (trifunctional protein),
alpha subunit is a protein...
- acetoacetyl-CoA
thiolase, beta-acetoacetyl
coenzyme A
thiolase, 2-methylacetoacetyl-CoA
thiolase [misleading], 3-oxothiolase,
acetyl coenzyme A
thiolase, acetyl-CoA...
- ketogenesis, two acetyl-CoA
molecules condense to form acetoacetyl-CoA via
thiolase. Acetoacetyl-CoA
briefly combines with
another acetyl-CoA via HMG-CoA synthase...
-
reductase HMG-CoA
synthase β-Hydroxybutyrate
dehydrogenase Mevalonate pathway Thiolase Unknown enzyme β-Hydroxybutyrate Acetoacetyl-CoA Acetyl-CoA Acetoacetate...
