-
Members of the
thiolase family can be
divided into two
broad categories:
degradative thiolases (EC 2.3.1.16) and
biosynthetic thiolases (EC 2.3.1.9). These...
-
names 3-oxothiolase deficiency,
Mitochondrial acetoacetyl-coenzyme A
thiolase deficiency, Alpha-methyl-acetoacetyl-CoA
thiolase deficiency Isoleucine...
-
enzyme subunit beta,
mitochondrial (TP-beta) also
known as 3-ketoacyl-CoA
thiolase, acetyl-CoA acyltransferase, or beta-ketothiolase is an
enzyme that in...
- Acetyl-CoA acetyltransferase, mitochondrial, also
known as acetoacetyl-CoA
thiolase, is an
enzyme that in
humans is
encoded by the ACAT1 (Acetyl-Coenzyme A...
- SCAD, MCAD, VLCAD, 3-hydroxyacyl-coenzyme A
dehydrogenase deficiency),
thiolase deficiency Mitochondrial myopathies:
deficiency of
succinate dehydrogenase...
- acetoacetyl-CoA
thiolase, beta-acetoacetyl
coenzyme A
thiolase, 2-methylacetoacetyl-CoA
thiolase [misleading], 3-oxothiolase,
acetyl coenzyme A
thiolase, acetyl-CoA...
-
mitochondrial also
known as hydroxyacyl-CoA dehydrogenase/3-ketoacyl-CoA
thiolase/enoyl-CoA
hydratase (trifunctional protein),
alpha subunit is a protein...
- dehydrogenase, enoyl-CoA hydratase, 3-hydroxyacyl-CoA dehydrogenase, and
thiolase. The
cycle produces a new
fatty acid
chain with two
fewer carbons and acetyl-CoA...
-
because the
liver lacks the
enzyme β-ketoacyl-CoA transferase, also
called thiolase.
Acetoacetate in low
concentrations is
taken up by the
liver and undergoes...
- 2NADH + FADH2
Condensation of pair of
acetyl CoA
molecules as
catalyzed by
thiolase.: 393 2Ac−CoA → AcCH2C(O)−CoA + H−CoA In mammals,
acetoacetate produced...
