- 3-
Methylglutaconyl-CoA hydratase, also
known as MG-CoA
hydratase and AUH, is an
enzyme (EC 4.2.1.18)
encoded by the AUH gene on
chromosome 19. It is a...
- methylcrotonyl-CoA
carboxylase to
methylglutaconyl-CoA (MG-CoA),
which is
subsequently converted to HMG-CoA by
methylglutaconyl-CoA hydratase. HMG-CoA is then...
- 3-
Methylglutaconyl-CoA (MG-CoA), also
known as β-
methylglutaconyl-CoA, is an
intermediate in the
metabolism of leucine. It is
metabolized into HMG-CoA...
-
include leucine, isoleucine, and valine. Its
immediate precursors are β-
methylglutaconyl-CoA (MG-CoA) and β-hydroxy β-methylbutyryl-CoA (HMB-CoA). HMG-CoA reductase...
- 3-Methylglutaconic
aciduria type I, 3-Methylglutaconic
acidemia or 3-
Methylglutaconyl-CoA
Hydratase Deficiency Mutations in the AUH gene
cause 3-methylglutaconic...
- β-Ketoisocaproic acid β-Ketoisocaproyl-CoA β-Leucine β-Methylcrotonyl-CoA β-
Methylglutaconyl-CoA β-Hydroxy β-methylglutaryl-CoA tryptophan→alanine→ N′-Formylkynurenine...
- acid
metabolism disorders,
among them 4-hydroxybutyric aciduria, 3-
methylglutaconyl-Co A
hydratase deficiency,
multiple carboxylase deficiency, methylmalonic...
- β-Ketoisocaproic acid β-Ketoisocaproyl-CoA β-Leucine β-Methylcrotonyl-CoA β-
Methylglutaconyl-CoA β-Hydroxy β-methylglutaryl-CoA tryptophan→alanine→ N′-Formylkynurenine...
- β-Ketoisocaproic acid β-Ketoisocaproyl-CoA β-Leucine β-Methylcrotonyl-CoA β-
Methylglutaconyl-CoA β-Hydroxy β-methylglutaryl-CoA tryptophan→alanine→ N′-Formylkynurenine...
- methylcrotonyl-CoA
carboxylase to
methylglutaconyl-CoA (MG-CoA),
which is
subsequently converted to HMG-CoA by
methylglutaconyl-CoA hydratase. HMG-CoA is then...
