- disease.
Hunter syndrome is
caused by a
deficiency of the
lysosomal enzyme iduronate-2-sulfatase (I2S). The lack of this
enzyme causes heparan sulfate and...
-
Iduronate 2-sulfatase (EC 3.1.6.13;
systematic name L-
iduronate-2-sulfate 2-sulfohydrolase) is a
sulfatase enzyme ****ociated with
Hunter syndrome. It...
- 000 births. MPS II,
Hunter syndrome or
iduronate sulfatase deficiency, is
caused by lack of the
enzyme iduronate sulfatase.
Hunter syndrome has two clinical...
- Arylsulfatase(A, B & G) O- and N-Sulfate
esters B-
Glucosamine (N-acetyl)-6-Sulfatase/GNS
Glycosaminoglycans C-
Iduronate 2-Sulfatase/IDS O- and N-Sulfate esters...
-
treat Hunter syndrome (also
called MPS-II). It is a
purified form of
iduronate-2-sulfatase, a
lysosomal enzyme, and is
produced by
recombinant DNA technology...
- \rightleftharpoons }
dermatan L-
iduronate Hence, this
enzyme has one substrate,
chondroitin D-glucuronate, and one product,
dermatan L-
iduronate. This
enzyme belongs...
-
Idiopathic sclerosing mesenteritis Idiopathic thrombocytopenic purpura Iduronate 2-sulfatase
deficiency IFAP
syndrome IgA
deficiency IgA
nephropathy IgA...
-
pyranoses are
stable in one of two
chair conformations 1C4 or 4C1. l-
iduronate is
different and
adopts more than one
solution conformation, with an equilibrium...
-
Initiative for
Democratic Socialism Institute for the
German Language Iduronate-2-sulfatase, a
sulfatase enzyme ****ociated with
Hunter syndrome Index...
-
membrane bound enzyme which hydrolyzes 3-beta-hydroxy
steroid sulfates;
iduronate 2-sulfatase EC 3.1.6.13 (IDS), a
lysosomal enzyme that
hydrolyzes the...
