-
Congenital hypofibrinogenemia is a rare
disorder in
which one of the
three genes responsible for
producing fibrinogen, a
critical blood clotting factor...
-
subclassified into four
distinct fibrinogen disorders: afibrinogenemia,
hypofibrinogenemia, dysfibrinogenemia, and hypodysfibrinogenemia.
Congenital afibrinogenemia...
- seen at
birth with
excessive hemorrhage from the navel.
Congenital hypofibrinogenemia is a rare
inherited disorder in
which blood may not clot normally...
-
orthostatic changes in
blood pressure and
heart rate
Fetal distress Hypofibrinogenemia (i.e., 50–250 mg/dL)
class 3:
Severe and
represents approximately...
- the
disorder causes abnormal bleeding and thrombosis.
Congenital hypofibrinogenemia, an
inherited disorder in
which blood may not clot
normally due to...
- pancytopenia,
liver dysfunction,
disseminated intravascular coagulation,
hypofibrinogenemia, hyperferritinemia, and hypertriglyceridemia.
Despite marked systemic...
- ecchymosis, erythemia, hypotension, tachycardia,
coagulopathy with
hypofibrinogenemia and thrombocytopenia, hematemesis, melena, epistaxis, hematuria, intracerebral...
-
effective diagnostic test for this condition. It is also
prolonged in
hypofibrinogenemia. In the
British comedy film
Doctor in the
House (1954), Sir Lancelot...
- can be used
concurrently to
distinguish anticoagulant effect from
hypofibrinogenemia or dysfibrinogenemia.
Normal values for
thrombin time may be 12 to...
-
nails Hypodontia of
incisors and
premolars Hypodysfibrinogenemia Hypofibrinogenemia,
familial Hypoglycemia with
deficiency of
glycogen synthetase in the...
