- 3-hydroxyisobutyrate dehydrogenase,
mitochondrial (
HIBADH) is an
enzyme that in
humans is
encoded by the
HIBADH gene. 3-Hydroxyisobutyrate
dehydrogenase catalyzes...
- HGNC:25842 Q6UWX4 7049 HHLA1 HGNC:4904 C9JL84 7050 HHLA2 HGNC:4905 Q9UM44 7051
HIBADH HGNC:4907 P31937 7052
HIBCH HGNC:4908 Q6NVY1 7053 HIC1 HGNC:4909 Q14526...
- HADHB, ACAA2);
Amino acid
catabolic pathways proteins (MCCC1, MCCC2, GLUD1,
HIBADH, CPS1);
Amino acid
biosynthesis proteins (PYCR1, PYCR2, ALDH18A1, SHMT2...
- interactions. NDUFB11
appears to
interact with FATE1, GPR42, CLDN7, GJB1,
HIBADH, EBP, GPR152, GPR101, TIMMDC1, TIMMDC1, PPBP, and CRELD2. GRCh38: Ensembl...
- death. It was
previously ****umed that 3-hydroxyisobutyrate
dehydrogenase (
HIBADH)
deficiency in the
valine catabolic pathway was the
underlying enzyme defect...