- HMG-CoA
reductase (3-hydroxy-3-methyl-
glutaryl-coenzyme A reductase,
official symbol HMGCR) is the rate-controlling
enzyme (NADH-dependent, EC 1.1.1.88;...
-
Glutaryl-CoA
dehydrogenase (GCDH) is an
enzyme encoded by the GCDH gene on
chromosome 19. The
protein belongs to the acyl-CoA
dehydrogenase family (ACD)...
- the
decarboxylation reaction. Finally,
glutaryl-CoA is
oxidatively decarboxylated to crotonyl-CoA by
glutaryl-CoA
dehydrogenase (E.C 1.3.8.6),
which goes...
-
Excessive levels of
their intermediate breakdown products (glutaric acid,
glutaryl-CoA, 3-hydroxyglutaric acid,
glutaconic acid) can ac****ulate and cause...
-
Glutaryl-coenzyme A is an
intermediate in the
metabolism of
lysine and tryptophan.
Glutaryl-CoA
dehydrogenase Rao KS,
Albro M,
Dwyer TM,
Frerman FE (Dec...
- 3-Hydroxy-3-methylglutaryl-CoA
lyase deficiency, (HMGCLD) also
known as
HMGCL deficiency, HMG-CoA
lyase deficiency, or
hydroxymethylglutaric aciduria,...
- lysine→
Saccharopine Allysine α-Aminoadipic acid 2-Oxoadipic acid
Glutaryl-CoA Glutaconyl-CoA Crotonyl-CoA β-Hydroxybutyryl-CoA leucine→ β-Hydroxy β-methylbutyric...
-
Glutaryl-CoA
dehydrogenase (non-decarboxylating) (EC 1.3.99.32, GDHDes,
nondecarboxylating glutaryl-coenzyme A dehydrogenase,
nondecarboxylating glutaconyl-coenzyme...
-
Glutaryl chloride or
pentanedioyl dichloride is an
organic compound with the
formula C5H6Cl2O2, or (CH2)3(COCl)2. It is the
diacid chloride derivative...
- the
mevalonate pathway by
partaking in the
synthesis of
hydroxymethyl glutaryl-CoA.
Acetylcholine synthesis: Acetyl-CoA is also an
important component...
