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Coproporphyrinogen-III oxidase,
mitochondrial (abbreviated as CPOX) is an
enzyme that in
humans is
encoded by the CPOX gene. A
genetic defect in the enzyme...
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acute hepatic porphyria. HCP is
caused by a
deficiency of the
enzyme coproporphyrinogen oxidase,
coded for by the CPOX gene, and is
inherited in an autosomal...
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Coproporphyrinogen III is a
metabolic intermediate in the
biosynthesis of many
compounds that are
critical for
living organisms, such as
hemoglobin and...
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Coproporphyrinogen I is an
isomer of
coproporphyrinogen III, a
metabolic intermediate in the
normal biosynthesis of heme. The
compound is not normally...
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Hereditary coproporphyria,
which is
characterized by a
deficiency in
coproporphyrinogen oxidase,
coded for by the CPOX gene, may also
present with both acute...
- In enzymology, a
coproporphyrinogen dehydrogenase (EC 1.3.99.22) is an
enzyme that
catalyzes the
chemical reaction coproporphyrinogen III + 2 S-adenosyl-L-methionine...
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Coproporphyrinogens are
tetrapyrroles with four
propionic acid
groups and an
equal number of
substituted methyls.
Coproporphyrinogen III is the most common...
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uroporphyrinogen III to
yield coproporphyrinogen III:
uroporphyrinogen III ⇌ {\displaystyle \rightleftharpoons }
coproporphyrinogen III + 4 CO2
Mutations and...
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Uroporphyrinogen III
Coproporphyrinogen III 1p34 4.1.1.37 176100
porphyria cutanea tarda,
hepatoerythropoietic porphyria Coproporphyrinogen III
oxidase Mitochondrion...
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synthase 2 (deficiency
causes sideroblastic/hypochromic anemia) CPOX:
coproporphyrinogen oxidase (deficiency
causes hereditary coproporphyria) FECH: ferrochelatase...
