Definition of Carnitines. Meaning of Carnitines. Synonyms of Carnitines

- oxidation have been identified. In case of fatty acid oxidation defects, acyl-carnitines ac****ulate in mitochondria and are transferred into the cytosol, and then...
- working. Most cell types appear to have transporters to import carnitine and export acyl-carnitines, which seems to be a mechanism to dispose of longer-chain...
- formation of acyl carnitines by catalyzing the transfer of the acyl group of a long-chain fatty acyl-CoA from coenzyme A to l-carnitine. The product is...
- Carnitine biosynthesis is a method for the endogenous production of L-carnitine, a molecule that is essential for energy metabolism. In humans and many...
- Carnitine palmitoyltransferase II deficiency, sometimes shortened to CPT-II or CPT2, is an autosomal recessively inherited genetic metabolic disorder...
- Carnitine O-palmitoyltransferase 2, mitochondrial is an enzyme that in humans is encoded by the CPT2 gene. Carnitine palmitoyltransferase II precursor...
- co-A is then exchanged with carnitine (via the enzyme carnitine palmitoyltransferase I) to produce a fatty acid-carnitine complex. This complex is then...
- fatty-acid metabolism disorders. Carnitine Transport Defect Carnitine-acylcarnitine translocase deficiency (CACT) Carnitine Palmitoyl Transferase I & II (...
- Carnitine-acylcarnitine translocase (CACT) is responsible for p****ive transport of carnitine and carnitine-fatty acid complexes and across the inner mitochondrial...
- Glycine propionyl-L-carnitine (GPLC) is a propionyl ester of carnitine that includes an additional glycine component. Due to tissues esterases enzymes...