-
BCKDH may
refer to: (3-methyl-2-oxobutanoate
dehydrogenase (2-methylpropanoyl-transferring))-phosphatase, an
enzyme 3-methyl-2-oxobutanoate dehydrogenase...
- The branched-chain α-ketoacid
dehydrogenase complex (BCKDC or
BCKDH complex) is a multi-subunit
complex of
enzymes that is
found on the mitochondrial...
-
acids involves the branched-chain alpha-keto acid
dehydrogenase complex (
BCKDH). A
deficiency of this
complex leads to a
buildup of the branched-chain...
-
dehydrogenase phosphatase, branched-chain α-keto acid
dehydrogenase phosphatase,
BCKDH', [3-methyl-2-oxobutanoate
dehydrogenase (lipoamide)]-phosphatase,...
-
pyruvate dehydrogenase complex, the α-ketoglutarate
dehydrogenase complex, the
BCKDH complex and the
glycine cleavage system (GCS),
among others.
Disorders in...
- SP-3164 [CRBN-IKZF3] (see also DRX-164) CR8 [CDK12-DDB1] PF-07208254 [BDK-
BCKDH E2] E7820 [DCAF15-RBM39, RBM23] [see also indisulam, tasisulam] SRI-41315...
- (Human) - BCAT1 gene & protein". www.uniprot.org.
Retrieved 2018-08-06. "
BCKDH in the BCAA
degradation pathway". Genome.jp.
August 6, 2018.
Retrieved August...
-
BCKDHB Identifiers Aliases BCKDHB, E1B, dJ279A18.1, BCKDE1B,
BCKDH E1-beta,
branched chain keto acid
dehydrogenase E1, beta polypeptide,
branched chain...
- that also
promotes BCKDK degradation by
promoting BCKDK interaction with
BCKDH-E2. A
variant of this molecule, PF-07328948, was
disclosed in 2024 and is...
-
inactivation of E1α
subunit of branched-chain
ketoacid dehydrogenase (
BCKDH). If a
patient has a
homozygous mutation (an
identical mutation in both...
