- acid
dehydratase (porphobilinogen synthase, or ALA dehydratase, or
aminolevulinate dehydratase) is an
enzyme (EC 4.2.1.24) that in
humans is
encoded by...
-
inhibitor Photosensitizers/PDT
Aminolevulinic acid
Efaproxiral Methyl aminolevulinate Padeliporfin Porphyrin derivatives (Porfimer
sodium Talaporfin Temoporfin...
- ; Ferreira,
Gloria C. (November 2011). "Molecular
enzymology of 5-
Aminolevulinate synthase, the
gatekeeper of heme biosynthesis".
Biochimica et Biophysica...
-
Methyl aminolevulinate (MAL) is a drug used as a
sensitizer in
photodynamic therapy. It is a
prodrug that is
metabolized to
protoporphyrin IX. It is marketed...
-
porphyria Inheritance Symptoms Prevalence Aminolevulinate dehydratase deficiency porphyria (ALADP) 5-
aminolevulinate dehydratase (ALAD)
Hepatic Autosomal recessive...
- \rightleftharpoons } 5-
aminolevulinate Hence, this
enzyme has one substrate, L-glutamate-1-semialdehyde, and one product, 5-
aminolevulinate. This
enzyme belongs...
-
Aminolevulinic acid
dehydratase deficiency porphyria (also
known as Doss porphyria, plumboporphyria, or ADP) is an
extremely rare
autosomal recessive metabolic...
- Hexaminolevulinate, sold
under the
brand name
Cysview among others, is an
imaging agent that
lights up
under blue
light during a blue
light cystoscopy...
- Delta-
aminolevulinate synthase 1 also
known as ALAS1 is a
protein that in
humans is
encoded by the ALAS1 gene. ALAS1 is an
aminolevulinic acid synthase...
-
causes ala-dehydratase
deficiency porphyria) ALAS1:
aminolevulinate, δ-,
synthase 1 ALAS2:
aminolevulinate, δ-,
synthase 2 (deficiency
causes sideroblastic/hypochromic...
